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Additionally, patients taking medications with significant drug interactions or those with conditions that could be exacerbated by changes in gastric emptying or metabolic function should be carefully evaluated by their prescribing provider

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Hyperammonemia occurs frequently in cases of impaired endogenous hepatic detoxification (e.g

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Neuronal ceroid lipofuscinoses (NCLs) are a group of autosomal-recessive hereditary lysosomal storage diseases caused by mutations in at least 8 genes (CLN1-CLN8) [115]

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Urology 48 , 835850 (1996)

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Sequential change of the levels of serum ammonia, valproic acid, free carnitine, acylcarnitine, total carnitine, ratios of acylcarnitine/free carnitine, and the scores of Brief Psychotic Rating Scale, Clinical Global Impression-Severity scale, and the Global Assessment of Functioning scale were compared within total subjects and two groups divided by the effectiveness of levocarnitine supplementation against baseline hyperammonemia

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